Hirschsprung disease

Document Type

Journal Article

Publication Date

1-1-2016

Journal

Fundamentals of Pediatric Surgery, Second Edition

DOI

10.1007/978-3-319-27443-0_62

Keywords

Aganglionosis; Duhamel; Enterocolitis; Hirschsprung disease; Pull-through; Soave; Transanal pull-through

Abstract

© Springer International Publishing AG 2011, 2017. Hirschsprung disease refers to congenital aganglionosis of some or all of the colon. Patients typically present with constipation early in life. The diagnosis and treatment of Hirschsprung disease has evolved over time but nearly always includes an operation to remove and replace the aganglionic bowel. These operations demand technical precision and a thoughtful approach. Patients with Hirschsprung disease also often require intensive and sometimes life-long follow-up care to achieve a successful outcome.

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