Uhl’s anomaly: A one and a half ventricular repair in a patient presenting with cardiac arrest

Authors

Reginald Chonoune
Adam Lowry
Karthik Ramakrishnan
Gail D. Pearson, George Washington University
Jeffrey P. Moak, George Washington UniversityFollow
Dilip S. Nath, George Washington University

Document Type

Journal Article

Study Type

casereport

Publication Date

2017

Journal

Journal of the Saudi Heart Association

DOI

10.1016/j.jsha.2017.03.011

Abstract

Uhl’s anomaly, first reported in 1952, is an extremely rare congenital cardiac defect characterized by partial or complete loss of the right ventricular myocardium and unknown etiology. Fewer than 100 cases have been described. The response to medical management is poor and there is no known ideal surgical approach or timing for treatment. We report the case of a previously active adolescent male presenting with cardiac arrest, who underwent successful bidirectional cavopulmonary anastomosis (“Glenn” anastomosis) with right atrial reduction and right ventricular free wall plication.

Comments

Reproduced with permission of Elsevier B.V. Journal of the Saudi Heart Association

Creative Commons License

This work is licensed under a Creative Commons Attribution-Noncommercial-No Derivative Works 4.0 License.

APA Citation

Chonoune, R., Lowry, A., Ramakrishnan, K., Pearson, G. D., Moak, J. P., & Nath, D. S. (2017). Uhl’s anomaly: A one and a half ventricular repair in a patient presenting with cardiac arrest. Journal of the Saudi Heart Association, (). http://dx.doi.org/10.1016/j.jsha.2017.03.011

Peer Reviewed

1

Open Access

1