Document Type
Journal Article
Study Type
casereport
Publication Date
2017
Journal
Journal of the Saudi Heart Association
DOI
10.1016/j.jsha.2017.03.011
Abstract
Uhl’s anomaly, first reported in 1952, is an extremely rare congenital cardiac defect characterized by partial or complete loss of the right ventricular myocardium and unknown etiology. Fewer than 100 cases have been described. The response to medical management is poor and there is no known ideal surgical approach or timing for treatment. We report the case of a previously active adolescent male presenting with cardiac arrest, who underwent successful bidirectional cavopulmonary anastomosis (“Glenn” anastomosis) with right atrial reduction and right ventricular free wall plication.
Creative Commons License
This work is licensed under a Creative Commons Attribution-Noncommercial-No Derivative Works 4.0 License.
APA Citation
Chonoune, R., Lowry, A., Ramakrishnan, K., Pearson, G. D., Moak, J. P., & Nath, D. S. (2017). Uhl’s anomaly: A one and a half ventricular repair in a patient presenting with cardiac arrest. Journal of the Saudi Heart Association, (). http://dx.doi.org/10.1016/j.jsha.2017.03.011
Peer Reviewed
1
Open Access
1
Comments
Reproduced with permission of Elsevier B.V. Journal of the Saudi Heart Association